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KMID : 0363220080460111538
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Korean Journal of Dermatology
2008 Volume.46 No. 11 p.1538 ~ p.1542
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A Case of Progressive Facial Hemiatrophy
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Kim Chi-Yeon
Oh Chee-Won
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Abstract
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Progressive facial hemiatrophy (PFH) was first described by Parry and Romberg and this is a rare disorder of an
unknown origin. PFH is characterized by slowly progressive, mostly unilateral facial atrophy of the skin, soft tissues,
muscles and underlying bony structures and is usually develops in the first or second decade of life. Although the
clinical presentation of PFH may appear similar to localized linear scleroderma en coup the sabre, some patients
presenting with PFH have neither en coup the sabre nor generalized sclerosis. Herein, we report on an unusual case
of a 7-year-old girl who presented with progressive hemiatrophy of the face.
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KEYWORD
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Progressive facial hemiatrophy, Scleroderma en coup de sabre
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